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Revista Médica Científica CAMbios

Periodicidad semestral: flujo continuo.

ISSN - Electrónico: 2661-6947 / DOI: 10.36015 • LILACS BIREME (19784); LATINDEX (20666)

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Keywords

Mediastinal Emphysema
Polymyositis
Subcutaneous Emphysema
Pulmonary Fibrosis
Dermatomyositis
Pneumothorax

How to Cite

1.
Spontaneous pneumomediastinum with spontaneous pneumothorax in a female patient with dermatomyositis: first case reported in our country and bibliographic review. Cambios rev. méd. [Internet]. 2019 Jun. 27 [cited 2025 Oct. 26];14(24):65-70. Available from: https://revistahcam.iess.gob.ec/index.php/cambios/article/view/215

Abstract

Introduction: pulmonary manifestations contribute significantly to morbidity and mortality of idiopathic inflammatory myopathies; such diseases encompass two large entities such as polymyositis (PM) and dermatomyositis (DM), which are a heterogeneous group of systemic autoimmune diseases, where the muscle is the target of an inappropriate immune-mediated destruction. Its main feature is muscle weakness and identification of underlying inflammation on muscle biopsy. Although the main target organ is skeletal muscle, skin and lungs, among other organs, are often affected by what are considered inflammatory myopathies systemic diseases. Pulmonary involvement is increasingly recognized as a serious complication and a frequent cause of morbidity and mortality in these diseases. Complications can mention pulmonary aspiration pneumonia, to hypoventilation, interstitial lung disease and deserves special mention spontaneous pneumomediastinum in patients with a previous diagnosis of both polymyositis (PM) and dermatomyositis (DM) who have reported around about 3 cases worldwide. The spontaneous pneumomediastinum (NE) is a clinical entity of unknown origin and benign that affects especially, but not exclusively, young people or individuals, it is sometimes explained by alveolar rupture caused by a peripheral parenchymal interstitial diseases producing honeycombing, without having a previous history of chest trauma. Case study: 52 year old female patient, single, residing in Guaranda (Province of Bolivar), with clinical history of dermatomiositosis (DM), diagnosed one month ago at the Reumotology Service of this Hospital and the moment was recieving prednisone 10 mg and 5 mg and 250 mg of chloroquine per day and 50mg/day of azatriopine.

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References

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