Periodicidad semestral: flujo continuo.
ISSN - Electrónico: 2661-6947 / DOI: 10.36015 • LILACS BIREME (19784); LATINDEX (20666)
these are: Hemophilia A, Hemophilia B and von Willebrand. Hemophilia is an inherited disorder, linked to the X chromosome, caused by absence or reduced activity of factor VIII or IX. Von Willebrand’s disease is caused by factor VIII deficiency. OBJECTIVE. Determine the demographic and epidemiological profile of patients with hemophilia
and von Willebrand. MATERIALS AND METHODS. Observational, descriptive, cross-sectional study. The study population was 133719 with a sample of 144 patients, the inclusion criteria were: patients of both sexes between 2 and 88 years of age, with
a diagnosis of Hemophilia A, B, von Willebrand. Attended in the external consultation of the Stomatology Area of the Carlos Andrade Marín Specialty Hospital, in the period 2015-2018. Data obtained from the AS400 system, analyzed in the International Business Machines Statistical Package for the Social Sciences program, Version 22.0.
RESULTS 77,0% (111; 144) belonged to the male gender. The age range was between 23 and 33 years with 24,0% (34; 144). They had hemophilia at 62,0% (93; 144); Hemophilia B 6,0% (9; 144); von Willerbrand 28,0% (42; 144). 50,0% (77; 144) received
dental treatments; preventive 15,0% (21; 144) and curative 13,0% (18; 144); being the biggest dental caries pathology. CONCLUSION. The demographic and epidemiological profile of patients with Hemophilia and von Willebrand was determined, which allowed to provide a comprehensive, interdisciplinary and timely treatment.
López Lopez S, Rodriguez O, Cruz N. Hemophilia A. Considerations for dental management of pediatric patients. J Oral Re s[Internet]. 2014 Aug[cited 2018 Augu 10];3(3):173-177. DOI: https://doi.org/10.17126/joralres.2014.041. Available from: http://www.jorales.com/index.php/JOR/article/view/joralres.2014.041
Matino D, Teitel J, Page D, Keepanasseril A, Iorio A, Irwin Walker. The haemophilia certification system in Canada. Blood Transfus [Internet]. 2014 Apr [cited 2018 Aug 10]; 12(3): 531-514. DOI 10.2450/2014.0032-14s . Available from: https://www.ncbi.nlm.nih.gov/pubmed/24922284
Cano MA, Ortiz GE, González SA. Cuidado odontológico de pacientes con trastornos hereditarios de la coagulación. CES odontol[Internet]. 2017 June [cited 2018 Aug 26];30(1):30-40. ISSN:0120-971X. Available from: http://www.scielo.org.co/scielo.php?script=sci_arttext&pid=S0120971X2017000100004&lng=en
Martínez-Rider R, Garrocho-Rangel A, Márquez-Preciado R, Bolaños-Carmona MV, Islas-Ruiz S, Pozos-Guillén A. Dental Management of a Child with Incidentally Detected Hemophilia: Report of a Clinical Case. Case Reports in Dentistry [Internet]. 2017 May 28[cited 2018 Aug 26];2017:1-5. DOI 10.1155/2017/7429738 . Available from: https://www.hindawi.com/journals/crid/2017/7429738/citations/
Soria J.Implementación de la clínica de atención integral para pacientes con hemofilia y otras alteraciones congénicas de la hemostasia en el Hospital Carlos Andrade Marin. Quito 2018[Tesis]. Repositorio digital USFQ[Internet];2018 Abr 17:1-62. Available from: http://repositorio.usfq.edu.ec/handle/23000/7144
Marega T, Golcalvez A, Urbini F. Odontología Especial. Quintessence[Editorial]. 2018 Abr[cited 2019 May];1:53-59. ISBN 978-85-7889-118-3.
Kalsi H, Nanayakkara L, Pasi KJ, Bowles L, Hart DP. Acess to primary dental care for patients with inherited bleeding disorders. Haemophilia [Internet]. 2011 Jul [cited 2018 Sep 11];18(4):510-515. DOI 10.1111/j.1365-2516.2011.02716.x. Available from: https://www.ncbi.nlm.nih.gov/pubmed/22151066
Kwon AY, Huh KH, Yi WJ, Symkhampha K, Heo MS, Lee SS, Choi SC. Haemophilic pseudotumour in two parts of the maxilla: case report. Dentomaxillofac Radiol[Internet]. 2016[cited Sep 11];45(6):20150440. DOI: 10.1259/dmfr.20150440. PMID: 27359071. Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5124770/
Bertamino M, Riccardi F, Banov L, Svahn J, Molinari A. Hemophilia Care in the Pediatric Age. J. Clin. Med[Internet]. 2017 May 19[cited 2018 Sep 13];6(5):54. DOI:https://doi.org/10.3390/jcm6050054. Available from: https://www.mdpi.com/2077-0383/6/5/54
Zaliuniene R, Peciuliene V, Brukiene V, Aleksejuniene J. Hemophilia and oral health. Stomatologija, Baltic Dental and Maxillofacial Journal [Internet]. 2014 Jan 01[cited 2018 October];16(4):127-131. PMID:25896036. Available from: https://europepmc.org/abstract/med/25896036
Abed H, Ainousa A. Dental management of patients with inherited bleeding disorders: a multidisciplinary approach. Gen Dent[Internet]. 2017 Nov-Dec[cited 2018 Sep 24];65(6):56-60. PMID:29099367. Available from: https://www.ncbi.nlm.nih.gov/pubmed/29099367
Organizacion Mundial de la salud. Salud bucodental. Biblioteca virtual de la OMS[Internet]. 2019 [cited 2018 Nov 10]. Available from: https://www.who.int/topics/oral_health/es/
Nuvvula S, Gaddam K, Kamatham R. Efficacy of tranexamic acid mouthwash as an alternative for factor replacement in gingival bleeding during dental scaling in cases of hemophilia: A randomized clinical trial. Contemp Clin Dent[Internet]. 2014 Jan[cited 2018 Nov 20];5(1):49-53. DOI: 10.4103/0976-237X.128663. Available from: https://www.ncbi.nlm.nih.gov/pubmed/24808695
Shastry SP, Kaul R, Baroudi K, Umar D. Hemophilia A: Dental considerations and management. J Int Soc Prev Community Dent[Internet]. 2014 Dec[cited 2018 Nov 20];4(3):147-52. DOI: 10.4103/2231-0762.149022. PubMed PMID: 25625071; PubMed Central PMCID: PMC4304051. Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4304051/
Skinner M, Soucie M, McLaughlin K. The National Haemophilia Program Standards, Evaluation and Oversight Systems in the United States of America. Blood Transfus [Internet]. 2014 Apr[cited 2018 Nov];12(3):542-548. DOI 10.2450/2014.0019-14s.Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4044795/
Salem K, Seyyedkhamesi S, Aminian M. Evaluación del estado de salud bucal y dental en niños y adolescentes hemofílicos en la ciudad de Rasht. J Pediatr Res[Internet]. 2018[cited 2018 Dec 10];5:182-186.. DOI 10.4274/jpr.80037. Available from: http://jpedres.org/archives/archive-detail/article-preview/evaluation-of-oral-and-dental-health-status-in-hem/21191
Babu NSV, Shah M, Patel P. Oral health status in children with haemophilia - a comparative study. J Haem Pract [Internet]. 2016 Abril [cited 2018 August]; 3(2): 1-5.1-5 DOI:10.17225/jhp00081. Available from: https://www.researchgate.net/publication/327193463_Oral_health_status_in_children_with_haemophilia_-_a_comparative_study
Salem K, Seyyedkhamesi S, Aminian M. Evaluation of Oral and Dental Health Status in Hemophilic Children and Adolescents in the City of Rasht. J Pediatr Res[Internet]. 2018 May[cited 2018 Dec 12];5(4): 182-186. Available from: DOI 10.4274/jpr.80037. Available from: https://pdfs.semanticscholar.org/9c0f/2a983f45a63df02046a3048619f4432cf532.pdf
.Grandas A. Niños con hemofilia y su atención odontológica por estomatología pediátrica. Revisión de la literatura / Children with Hemophilia and their Dental Care by Pediatric Stomatology. Review of Literature. UO [Internet]. 2016 Jun 18[cited 2019 Jan 10];35(74):113-26. DOI: https://doi.org/10.11144/Javeriana.uo35-74.nhao. Available from: https://revistas.javeriana.edu.co/index.php/revUnivOdontologica/article/view/17212
Dudeja PG, Dudeja KK, Lakhanpal M, Ali S. Endodontic management of a haemophilic patient- a clinical perspective. J Clin Diagn Res[Internet]. 2014 Jul[cited 2019 Jan 10];8(7):17-8. DOI: 10.7860/JCDR/2014/8404.4592. Epub 2014 Jul 20. PubMed PMID: 25177652; PubMed Central PMCID: PMC4149158. Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4149158/
The authors who publish in this journal accept the following conditions:
1. The authors retain the copyright and grant to the CAMbios MEDICAL-SCIENTIFIC JOURNAL HECAM the right of the first publication, with the work registered with the Creative Commons attribution license, which allows third parties to use the published material provided that they mention the authorship of the work and the first publication in this journal.
2. Authors can make other independent and additional contractual agreements for the non-exclusive distribution of the version of the article published in this journal (for example, include it in an institutional repository or publish it in a book) as long as it clearly indicates that the work was published. for the first time in the CAMbios MEDICAL-SCIENTIFIC JOURNAL HECAM.
